CHEBI:55534 - (R)-2-hydroxy-4-methylpentanoic acid

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ChEBI Name (R)-2-hydroxy-4-methylpentanoic acid
ChEBI ID CHEBI:55534
ChEBI ASCII Name (R)-2-hydroxy-4-methylpentanoic acid
Definition The (R)-enantiomer of 2-hydroxy-4-methylpentanoic acid. Found in patients with short-bowel syndrome (an inborn error of metabolism), and in maple syrup urine disease, MSUD.
Stars This entity has been manually annotated by the ChEBI Team.
Supplier Information
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Formula C6H12O3
Net Charge 0
Average Mass 132.15770
Monoisotopic Mass 132.07864
InChI InChI=1S/C6H12O3/c1-4(2)3-5(7)6(8)9/h4-5,7H,3H2,1-2H3,(H,8,9)/t5-/m1/s1
InChIKey LVRFTAZAXQPQHI-RXMQYKEDSA-N
SMILES CC(C)C[C@@H](O)C(O)=O
Roles Classification
Chemical Role(s): Bronsted acid
A molecular entity capable of donating a hydron to an acceptor (Bronsted base).
(via oxoacid )
Biological Role(s): metabolite
Any intermediate or product resulting from metabolism. The term 'metabolite' subsumes the classes commonly known as primary and secondary metabolites.
(via 2-hydroxy-4-methylvaleric acid )
View more via ChEBI Ontology
ChEBI Ontology
Outgoing (R)-2-hydroxy-4-methylpentanoic acid (CHEBI:55534) is a (2R)-2-hydroxy monocarboxylic acid (CHEBI:17893)
(R)-2-hydroxy-4-methylpentanoic acid (CHEBI:55534) is a 2-hydroxy-4-methylvaleric acid (CHEBI:59783)
(R)-2-hydroxy-4-methylpentanoic acid (CHEBI:55534) is conjugate acid of (R)-2-hydroxy-4-methylpentanoate (CHEBI:55535)
(R)-2-hydroxy-4-methylpentanoic acid (CHEBI:55534) is enantiomer of (S)-2-hydroxy-4-methylpentanoic acid (CHEBI:44510)
Incoming (R)-2-hydroxy-4-methylpentanoyl-CoA (CHEBI:87433) has functional parent (R)-2-hydroxy-4-methylpentanoic acid (CHEBI:55534)
(R)-2-hydroxy-4-methylpentanoate (CHEBI:55535) is conjugate base of (R)-2-hydroxy-4-methylpentanoic acid (CHEBI:55534)
(S)-2-hydroxy-4-methylpentanoic acid (CHEBI:44510) is enantiomer of (R)-2-hydroxy-4-methylpentanoic acid (CHEBI:55534)
IUPAC Name
(2R)-2-hydroxy-4-methylpentanoic acid
Synonyms Sources
(R)-2-hydroxy-4-methylpentanoic acid ChEBI
(R)-2-hydroxy-4-methylvaleric acid ChEBI
(R)-2-hydroxyisocaproic acid ChEBI
(R)-leucic acid ChEBI
2-hydroxy-4-methyl-D-valeric acid ChEBI
alpha-Hydroxyisocaproic acid ChEBI
D-2-hydroxy-4-methylpentanoic acid ChEBI
D-2-hydroxy-4-methylvaleric acid ChEBI
D-2-hydroxyisocaproic acid ChEBI
D-leucic acid ChEBI
delta-leucic acid ChEBI
leucic acid ChEBI
Manual Xref Database
C03264 KEGG COMPOUND
View more database links
Registry Numbers Types Sources
1721731 Beilstein Registry Number Beilstein
20312-37-2 CAS Registry Number KEGG COMPOUND
Citation Waiting for Citations Type Source
9766851 PubMed citation Europe PMC
Last Modified
21 August 2017